What is Duane syndrome?
Duane syndrome, also called Duane retraction syndrome (DRS), is a group of eye muscle disorders that cause abnormal eye movements. People with Duane syndrome have difficulty rotating one or both eyes outward (abduction) or inward (adduction).
What is the cause of Duane Syndrome?
Duane syndrome is due to miswiring of the eye muscles. In Duane syndrome, the sixth cranial nerve that controls the lateral rectus muscle (the muscle that rotates the eye out towards the ear) does not develop properly. dfThus, the problem is not primarily with the eye muscle itself, but with the nerve that transmits the electrical impulses to the muscle. There is also irregular innervation of a branch from the third cranial nerve, which controls the medial rectus muscle (the muscle that rotates the eye toward the nose). This is why abnormalities may be found in both left gaze and right gaze.
Who gets Duane syndrome?
Duane syndrome affects girls more often than boys. In addition, the left eye is more likely than the right eye to be affected. The reason for this is not known. Around 20% of Duane syndrome patients have both eyes affected. No particular race or ethnic group is more likely to be affected.
What are the other characteristics of Duane syndrome?
Squint, Abnormala head posture, Amblyopia (Lazy eye), Narrowing of palpebral fissure or smaller looking eye and abnormal upward or downward movements of eye.
Is Duane syndrome congenital (present from birth)?
Duane retraction syndrome is present from birth, even if it is not recognized during infancy. An abnormal head posture and strabismus are often visible in old photographs taken in early childhood.
When do we treat Duane syndrome?
Surgery for Duane syndrome is indicated for one of four reasons:
To reduce the squint
To eliminate a socially unacceptable head position
To eliminate a significant upshoot or downshoot
To eliminate disfiguring enophthalmos (Smaller looking eye).